발행물

전체 논문

190

1

Multi-omic analysis of selectively vulnerable motor neuron subtypes implicates altered lipid metabolism in ALS
Lee H, Lee JJ, Park NY, Dubey SK, Kim T, Ruan K, Lim SB, Park SH, Ha S, Kovlyagina I, Kim KT, Kim S, Oh Y, Kim H, Kang SU, Song MR, Lloyd TE, Maragakis NJ, Hong YB*, Eoh H*, Lee G*
Nat Neurosci, 2021

2

Graphene quantum dots attenuate TDP-43 proteinopathy in amyotrophic lateral sclerosis.
Park NY, Heo Y, Yang JW, Yoo JM, Jang HJ, Jo JH, Park SJ, Lin Y, Choi J, Jeon H, Cha SJ, Bae G, Kim D, Kim J, Zeno W, Park JB, Isozumi N, Saio T, Kim SHy, Lee H, Hong BH, Nahm M, Lee YH, Hong YB
ACS Nano, 2025

3

Transcriptional control of motor pool formation and motor circuit connectivity by the LIM-HD protein Isl2.
Lee Y, Yeo IS, Kim N, Lee DK, Kim KT, Yoon J, Yi J, Hong YB, Choi BO, Kosodo Y, Kim D, Park J, Song MR
eLife, 2023

4

PINK1 and Parkin rescue motor defects and mitochondria dysfunction induced by a patient-derived HSPB3 mutant in Drosophila models.
Han JE, Kang KH, Kim H, Hong YB, Choi BO, Koh H
Biochem Biophys Res Commun, 2023

5

TGFβ4 alleviates the phenotype of Charcot-Marie-Tooth disease type 1A.
Jeon H*, Jang SY*, Kwak G*, Yi YW*, You MH*, Park NY*, Jo JH, Yang JW, Jang HJ, Jeong SY, Moon SK, Doo HM, Nahm M, Kim D, Chang JW, Choi BO, Hong YB
Brain, 2023

6

PINK1 and Parkin Ameliorate the Loss of Motor Activity and Mitochondrial Dysfunction Induced by Peripheral Neuropathy-Associated HSPB8 Mutants in Drosophila Models.
Kang KH, Han JE, Kim H, Kim S, Hong YB, Yun J, Nam SH, Choi BO, Koh H
Biomedicines, 2023

7

COUP-TFII plays a role in cAMP-induced Schwann cell differentiation and in vitro myelination by upregulating Krox20.
Han SH, Kim YH, Park SJ, Cho JG, Shin YK, Hong YB, Yun J, Han JY, Park HT, Park JI
J Neurochem, 2023

8

Cytokines secreted by mesenchymal stem cells reduce demyelination in an animal model of Charcot-Marie-Tooth disease.
Jeon H*, Kim HJ*, Doo HM*, Chang EH, Kwak G, Mo WM, Jang SY, Lee MW, Choi BO, Hong YB
Biochem Biophys Res Commun, 2022

9

Phenotypic heterogeneity in patients with NEFL-related Charcot-Marie-Tooth disease.
Kim HJ, Kim SB, Kim HS, Kwon HM, Park JH, Lee AJ, Lim SO, Nam SH, Hong YB, Chung KW, Choi BO
Mol Genet Genomic Med, 2022

10

Multi-omic analysis of selectively vulnerable motor neuron subtypes implicates altered lipid metabolism in ALS.
Lee H, Lee JJ, Park NY, Dubey SK, Kim T, Ruan K, Lim SB, Park SH, Ha S, Kovlyagina I, Kim KT, Kim S, Oh Y, Kim H, Kang SU, Song MR, Lloyd TE, Maragakis NJ, Hong YB*, Eoh H*, Lee G*
Nat Neurosci, 2021